Pulmonary hypertensive necrotizing arteritis: An unusual case of unilateral involvement in an infant with congenital heart disease
2010
Abstract
Pulmonary hypertension (PH) is defined clinically as a pulmonary artery pressure greater than 25 mmHg at rest or greater than 30 mmHg during exercise. In 1958, Heath and Edwards developed a 6-grade scheme for sequential analysis of pulmonary vascular alterations encountered in PH; the severe irreversible lesions (gr. 4,5,6) comprise plexiform lesions, angiomatoid lesions, and fibrinoid necrosis/arteritis.
We report a unique case of an infant with congenital heart disease with the finding of necrotizing arteritis affecting only one lung.