IgA pemphigus associated with monoclonal gammopathy completely resolved after achievement of complete remission of multiple myeloma with bortezomib, cyclophosphamide and dexamethasone regimen

Abstract

Monoclonal gammopathy-associated IgA pemphigus is a debilitating skin disorder with inconsistent response to treatment. A 61-year-old woman with IgA pemphigus and monoclonal gammopathy of unknown significance had been treated unsuccessfully with cyclophosphamide/dexamethasone and then with rituximab.

Keywords

• IgA pemphigus
• subcorneal pustular dermatosis
• bortezomib
• rituximab
• monoclonal gammopathy
• subcorneal pustular dermatosis
• spectrum
• disease