Abstract
We describe case history of 25 years old woman with pulmonary form of neuroendocrine tumor. There was overproduction of ACTH (adenocorticotropic hormon) resulting in Cushings syndrome.
After the surgery we detected residual tumor in mediastinum with relapsing hormonal symptoms. Therefore we started the systemic treatment with somatostatin analogs.
The disease became resistant after 3 years and therefore was the patient indicated for bilateral adrenalectomy. Despite of very good clinical outcome the primary tumor remains in mediastinum and the further treatment remains problematic.