PFAPA syndrome: clinical characteristics and treatment outcomes in a large single-centre cohort

Abstrakt

We offer diagnostic and therapeutic algorithms that have proven effective during this prospective trial. Our findings support the general belief of benign nature of this aetiologically unclear condition, despite proportion of patients having persistent disease for years.

Maintenance of normal findings in afebrile intervals, striking response to a single dose of prednisone and normal growth and development together with spontaneous tendency towards prolongation of afebrile intervals are important confirmatory of PFAPA syndrome.

Klíčová slova

• PFAPA
• syndrome
• clinical
• characteristics
• treatment
• outcomes
• large
• single-centre
• cohort