Treatment of Posterior Persistent Hyperplastic Primary Vitreous Complicated by Tractional Retinoschisis in an Adult
Abstract
This case report deals with a rare case of posterior persistent hyperplastic primary vitreous (PHPV) that was successfully treated in an adult by scleral buckling using a silicone implant, pars plana vitrectomy, and laser coagulation. Persistent hyperplastic primary vitreous is a congenital anomaly caused by abnormal development of the eye, manifesting by strabismus, leukocoria, and poor vision.
It is usually diagnosed in early childhood, and no report of its initial diagnosis in an adult has been found. Secondary complications are vitreous hemorrhage, tractional retinal detachment, secondary glaucoma, and phthisis bulbi. 1,2 Usually unilateral, PHPV can occur at the anterior site of the vitreous (called the anterior form), at the posterior site of the vitreous (called the posterior form), or at both sites.
Purely posterior PHPV, the form seen in our patient, is rare. Bilateral PHPV is also rare.