Plexiform neurofibromas of the orbit are often a complicated problem. Although surgical treatment is not certainly the most demanding performance, a gradual progression is inevitable in most cases leads to a not entirely satisfactory results.
Partial resections of the tumor may improve the exopthalmus and reduce the risk of high intraocular pressure. Unfortunately, stopping the loss of visual acuity is often only temporary.
Supraorbital craniotomy with removal of the superciliary arch and the orbit ceiling is suitable for lesions in the upper orbit and apex area7. Careful reconstruction of the individual layers of the surgical field after removal of the tumor will ensure the patient a good cosmetic effect and good primary healing of the wound.