Successful Treatment of a Newborn With Genetically Confirmed Long QT Syndrome 3 and Repetitive Torsades De Pointes Tachycardia

Abstract

Neonatal manifestations of long QT syndrome are associated with a high risk of sudden cardiac death. A 2-day-old term newborn was admitted with signs of dysrhythmia.

Fetal echocardiography ahowed structural normal heart anatomy. After administration the patient developed two episodes of torsade de pointes tachycardia, requiring cardiopulmonary resuscitation, direct defibrilation and intravenous beta blockade wit esmolol.

Follow up studies showed normal development.

Keywords

• newborns, dyssrhytmias, torsede de pontes, resuscutation
• beta-blockers
• esmolol