Primary pulmonary hypertension in connective tissue diseases

Abstract

Pulmonary arteriální hypertension is common in systemic sclerosis and systemic lupus erythematosus, though very contradictory reports are about rheumatoid arthritis, sarcoidosis, poly/dematomyositis, mixed connective tissue disease and Sjögren's syndrome.

Keywords

• pulmonary arterial hypertension
• systemic sclerosis
• systemic lupus erythematosus
• transthoracic echocardiography
• right heart catheterisation