Low-grade myofibroblastic sarcoma (LGMS) is a very rare, atypical myofibroblastic tumor with fibromatosis-like features with predilection mostly in head and neck region. LGMS occurs primarily in adult patients with a slight male predominance.
Only few cases of LGMS affecting the larynx have been reported in literature to this date. The authors describe a case of low-grade myofibroblastic sarcoma of the larynx in a 40-year-old male patient.
The clinicopathological characteristics, immunohistochemical findings and treatment are discussed.