Idiopatic pulmonary fibrosis (IPF) is a serious treatable disease of variable course and lethal prognosis. Presented case report reviews case of the patient, who was treated for many years by inhaled corticosteroids despite known fibrotic interstitial lung involvement detected by computed tomography.
This case happened in the era of antifibrotic treatment, which could have been used for Czech IPF patients since 2011. The patient underwent in 2014 acute exacerbation of the disease and he died of this exacerbation.
Further discussion involves possible impact of both medical and patients oriented approach to IPF course, especially with regards to early diagnosis and treatment options.