Abstract
Hereditary angioedema (HAE) is a rare disease that is characterized by the formation of itchy swelling of the subcutis and mucous membranes and, according to the location of the angioedema, may endanger the patient's life. Although awareness of rare disease is increasing, HAE still escapes early diagnosis.
HAE is one of the immunodeficiency states with qualitative or quantitative lack of C1-inhibitor.