Publication at First Faculty of Medicine, Faculty of Physical Education and Sport, Second Faculty of Medicine |
2020
Abstract
3-10% patients with congenital heart disease (CHD) develop pulmonary arterial hypertension (PAH). The natural course of untreated CHD with significant left-to-right shunt is gradual increase in pulmonary vascular resistance, eventually resulting in reversal of the shunt (Eisenmenger syndrome, ES).
PAH-CHD is associated with significant morbidity and mortality. Due to early diagnosis and surgical possibilities of CHD repair, there has been a significant decrease in number of patients with ES.
Authors present a case report of a fifteen-year-old boy with ES and a life-threatening complication - multiplex septic intracranial embolisation.