Abstract
Cystic fibrosis (CF) is a severe age-progressive autosomal recessively inherited multiorgan disease. The essence of the therapeutic approach to patients with CF is the effort to maximally compensate for the underlying disease, prevention and early treatment of complications.
Acute exacerbations of the underlying disease or pneumonia are a common cause of respirátory deterioration, but it is also necessary to look for the rarer causes of dyspnea as a differential diagnosis. CF is one of the diseases with a higher risk of cardiovascular disease.
The most common cardiovascular complication is cor pulmonale. Since adolescence, pulmonary embolism has been one of the causes of acute dyspnea, sometimes with an image of acute cor pulmonale, as evidenced by the presented case report of an 18.5-year-old girl.