Publication at Second Faculty of Medicine |
2020
Abstract
Idiopathic pulmonary fibrosis is a chronic progressive, fibrotic lung disease that is currently treatable. The approach to treatment should be comprehensive.
The pharmacological basis of therapy is the antifibrotic preparations pirfenidone and nintedanib, if the patient meets the treatment criteria. We also include other forms of therapy, especially respiratory rehabilitation, nutritional support, oxygen therapy, psychotherapy and lung transplantation.
Mortality of the disease is still high, the median survival time without treatment is 3-5 years, with treatment the time doubles. Palliative medicine is part of a comprehensive approach to the patient.