Congenital pulmonary airway malformation (CPAM) with its incidence 1:25-35 000 belongs to the most frequent congenital lung anomalies. Pulmonary sequestration (PS) occures less often.
These malformations can be mixed sometimes, called hybrid lesions. They need to be correctly diagnosed in patients with unknown pulmonary lesions of any age.
They can be easily diagnosed prenatally by ultrasonography. Clinical presentation differs from asymptomatic lesions to respirátory failure of child.
Therapeutic approach depends on symptoms, size and type of the malformation as well as personal experience.