Defective kinetics of cytochrome c oxidase and alteration of mitochondrial membrane Potential in fibroblats and cytoplasmic hybrid cells with the mutation for myoclonus Epilepsy with ragged-red fibres ( MERRF) at position 8344 nt.

Abstrakt

Cytofluorimetry,mitochondrial diseases,OXPHOS (oxidative phosphorylation), TMRM (tetramethylrhodamine methyl ester).